Journal of the Bahrain Medical Society
Year 2021, Volume 33, Issue 4, Pages 38-42
https://doi.org/10.26715/JBMS.33_2021_4_9Suad Rashid Al Amer1, Vimalarani Arulselvam2*, Rajesh Jayakumar3, Abhinav Agarwal4, Neale Nicola Kalis5
1Consultant,Department of Pediatric Cardiolgy, Mohammed bin Khalifa bin Salman Al-Khalifa Cardiac Center, Bahrain Defense Forces Hospital, Kingdom of Bahrain.Senior Lecturer, Royal College of Surgeons of Ireland – Medical University of Bahrain (RSCI-MUB).
2Chief Resident, Department of Pediatric Cardiology, Mohammed bin Khalifa bin Salman Al-Khalifa Cardiac Center, Bahrain Defense Forces Hospital, Kingdom of Bahrain.
3Chief Resident, Department of Cardiology, Mohammed bin Khalifa bin Salman Al-Khalifa Cardiac Center, Bahrain Defense Forces Hospital, Kingdom of Bahrain.
4Senior Resident, Department of Pediatric Cardiology, Mohammed bin Khalifa bin Salman Al-Khalifa Cardiac Center, Bahrain Defense Forces Hospital, Kingdom of Bahrain.
5Consultant,Department of Pediatric Cardiolgy, Mohammed bin Khalifa bin Salman Al-Khalifa Cardiac Center, Bahrain Defense Forces Hospital, Kingdom of Bahrain.Professor in Pediatrics, Royal College of Surgeons of Ireland – Medical University of Bahrain (RSCI-MUB).
*Corresponding author: Dr.Vimalarani Arulselvam, MBBS, DNB(Ped), FNB (Ped Card)Mohammed bin Khalifa bin Salman Al-Khalifa Cardiac Center, Road 4524,Block 945, Al Rifa Wa Al Mintaqah, Awali. Kingdom of Bahrain. Tel: + (973) 17889935/3211902. E-mail: drvimala24@gmail
Received date: July 21, 2021; Accepted date: December 02, 2021; Published date: December 31, 2021
Abstract
Congenital kinking of aorta or pseudocoarctation is a rare anomaly of the aortic arch with elongation and kinking of aorta at the level of ligamentum arteriosum. This anomaly is not a true coarctation as there is no significant hemodynamic obstruction or pressure gradient across the lesion. We report two cases with this anomaly diagnosed during the evaluation for incidental finding of murmur. Both patients had flow gradient across the kinked segment of aorta by echocardiography but did not require any intervention. Long term complication is aneurysmal dilatation and rupture beyond the kinked segment. Computed tomography of the aorta is a simple noninvasive diagnostic modality for the definitive diagnosis. Surgical repair should be performed for all symptomatic individuals. Regular periodic follow up is mandatory for all asymptomatic patients.
Keywords: Aortic arch syndromes, Aortic coarctation, Congenital heart defects, Echocardiography, Thoracic aorta